The ideal treatment strategy for pulmonary sequestration whether resection or embolization in childhood is not clearly defined. Although extralobar pulmonary sequestration eps is a rare congenital lung anomaly, it is the second most common lung malformation in children, accounting for 0. Extralobar pulmonary sequestrations may be located in intrathoracic or extrathoracic areas. Uniportal videoassisted thoracoscopic surgery lobectomy. It is typically classified into intralobar and extralobar sequestration. Anomalous pulmonary artery from the aorta associated with. Pulmonary sequestration is a nonfunctioning lung mass with an abnormal connection to tracheobronchial trees and an anomalous systemic artery supply. Imaging of extralobar pulmonary sequestration in a patient. Although sequestrations are asymptomatic, they may become symptomatic by events such as infection, degeneration and trauma. Sihoe, qigang luo, guangqiang shao, yue li, jinglong li and dazhi pang abstract background. This pdf is available for free download from a site hosted by medknow publications.
Unique extralobar sequestration with atypical location and aberrant vessels. Bronchopulmonary sequestration is a relatively rare medical condition wherein a mass of nonfunctioning primitive lung tissue does not communicate with the tracheobronchial tree and receives its blood supply from an anomalous systemic artery. Pulmonary sequestration is a congenital anomaly resulting in nonfunctioning pulmonary tissue with no. The mass was attached to the right pulmonary artery by a fibrovascular pedicle which contained a small elastic artery, veins, and nerve bundles. Loe pulmonar con seccion medular problema n 1 loe pulmonar. Semiologia radiologica basica pulmonar patron alveolar ocupacion del espacio aereo pulmonar sangre, pus, agua, cel. Extrathoracic intradiaphragmatic extralobar pulmonary sequestrations are an extremely rare subset of bronchopulmonary sequestrations and there have been very few reported cases until now.
Stem cell therapy for idiopathic pulmonary fibrosis. Infarction of an extralobar pulmonary sequestration in a. Author links open overlay panel toshihiro osaki md a mantaro. The patient continued to do well and remained pneumonia free. A case report, journal of pediatric surgery on deepdyve, the largest online rental service for scholarly research with thousands of academic publications available at your fingertips. There was a leftsided variant of the extralobar type with double systemic arterial blood supply, single systemic venous drainage, and an incomplete bronchial tree for. Pulmonary sequestration is a rare congenital pulmonary disorder defined as an area of dysplastic and nonfunctioning pulmonary tissue with an anomalous systemic blood supply. Read upper thoracic extralobar pulmonary sequestration with anomalous blood supply from the subclavian artery, journal of pediatric surgery on deepdyve, the largest online rental service for scholarly research with thousands of academic publications available at your fingertips. This is a report of a patient with an infarcted extralobar pulmonary sequestration, an unusual complication of an uncommon entity. Bilateral sequestrations were rareonly three cases had been reported. Infarction of torsed extralobar pulmonary sequestration in. Pulmonary sequestration intralobar radiology reference.
The observation, as in the present patient, of intralobar right and extralobar left sequestrations is even more uncommon. Case report open access uniportal thoracoscopic lobectomy for intralobar pulmonary sequestration alan d. Bronchopulmonary sequestration is the term given to a region of lung parenchyma that is partially or completely. This discussion is concerned with the roentgen diagnosis of an anomalous systemic artery to the lung associated with congenital cystic pulmonary abnormalities. Survival of chinese patients with pulmonary arterial. The sequestered lung was completely excised using a videoassisted thoracoscopic approach. While the diagnosis of es can be done in 60% of the cases in the first decade of life this could be achieved for only half of the patients with is cases. Patients usually present before the third decade with recurrent infection. The mass was identified to be an extralobar pulmonary sequestration. Pulmonary sequestration is an uncommon congenital condition for which surgical resection is usually indicated either via open thoracotomy or conventional multiport videoassisted thoracoscopic surgery vats. Videoassisted thoracoscopic surgery revealed the mass to be a rare case of extralobar pulmonary sequestration that had undergone infarction. Diagnosis of intraabdominal extralobar pulmonary sequestration by means of ultrasound in a neonate. We describe a 48yearold korean woman found to have left peridiaphragmatic lesion on computed.
Abstracta laparoscopic transperitoneal approach allowed for. Secuestro pulmonar extralobar asociado a malformacion adenomatoide quistica tipo 2 1. Extralobar lung sequestration associated with fatal. Pulmonary sequestration extralobar radiology reference. Coil occlusion of aberrant arteries to pulmonary sequestration in a case with pulmonary atresia with intact ventricular septum. Abstractextralobar pulmonary sequestrations may be located in intrathoracic or extrathoracic. Our institution has no clear policy, therefore both therapies are performed.
Intradiaphragmatic extralobar pulmonary sequestration in. Mar 11, 2014 este video versa sobre hdc patitas cortas. Thoracoscopic resection of intra and extralobar pulmonary sequestration in the first 3 months of life. We report a unique extralobar pulmonary sequestration in the upper thoracic region with 3 aberrant. Pulmonary sequestration is an uncommon congenital condition for which surgical resection is usually. Intralobar pulmonary sequestration is located within the visceral pleura and is surrounded by normal lung, whereas extralobar pulmonary sequestration is separated from the lung by a pleural envelope. It is usually encountered in infants, most being diagnosed before six months. If you continue browsing the site, you agree to the use of cookies on this website. However, during pulmonary resection, inadvertent injury of the aberrant artery can cause a lifethreatening hemorrhage.
Infarcted pulmonary sequestration of either type has not been described previously. Surgical resection is the standard of care for both intralobar and extralobar pulmonary sequestration. Pdf extralobar pulmonary sequestration with combined. Two types of pulmonary sequestration are recognized. Endovascular treatment of pulmonary sequestration with. Unilateral coexisting intralobar and extralobar pulmonary sequestrations. Of the two types of sequestration, intralobar sequestration is technically more challenging to resect. Excel individual calculator a version of the desktop software has been developed as an excel macro excel sheet calculator this runs gli calculations on an excel database. Unique extralobar sequestration with atypical location and. Extralobar sequestration of lung in newborn infant jama. Bronchopulmonary sequestration presenting as a spontaneous.
Secondary diaphragmatic eventration after resection of. Upper thoracic extralobar pulmonary sequestration with. Pulmonary sequestration ps is a rare congenital malformation of the lower respiratory tract, and the standard treatment of the disease has been conventional surgery with resection of abnormal parenchyma. Several es cases existing in the right and left hemithorax upper zones are cited in the literature. Seven cases proved by surgical resection and subsequent pathologic examination form the basis of the study. In a previous study of chinese patients with idiopathic pulmonary arterial hypertension ipah in the nontargeted therapy era, we reported 1 and 3year survival. Prenatal diagnosis of an extralobar pulmonary sequestration. Thoracoscopic resection of intra and extralobar pulmonary. There are two subtypes of pulmonary sequestration, namely intralobar sequestration ils and extralobar sequestration els. An incidental finding is described of extralobar sequestration of the lung in a nigerian child, presenting as an anterior mediastinal polycystic mass. Els is covered by its own pleura and this is what differentiates els from ils.
Extralobar pulmonary sequestration is a rare congenital in order to allow the paresis of the phrenic nerve to be. Read preoperative diagnosis of extralobar pulmonary sequestration with unusual vasculature. The radiological and pathological findings of lung sequestration in a premature infant are described. The noun sequestrum has wellknown orthopedic connotations and is defined in stedmans medical dictionary as a piece of necrosed bone which has become separated from the surrounding healthy osseous tissue. Slideshare uses cookies to improve functionality and performance, and to provide you with relevant advertising. Pulmonary sequestration is a rare congenital present from birth malformation where nonfunctioning lung tissue is separated from the rest of the lung and supplied with blood from an unusual source, often an artery from systemic circulation. Prenatal diagnosis of fetal intraabdominal extralobar. Lactante vomitador estenosis hipertrofica del piloro is the property of its rightful owner. This article is from journal of cardiothoracic surgery, volume 9. A pulmonary sequestration is a medical condition wherein a piece of tissue that ultimately develops into lung tissue is not attached to the pulmonary arterial blood supply, as is the case in normally developing lung. The sequestration of pulmonary tissue has been defined by potter1 to be masses of pulmonary tissue which have no communication with the bronchial tree. Extralobar sequestration of lung in newborn infant. The lesion typically manifests in the newborn period or early infancy with symptoms of respiratory distress.
The patient is symptom free at 41 months after this secondary procedure. Pulmonary sequestration is a congenital syndrome characterized by abnormal systemic blood supply to the lung, usually the lower lobe. Unilateral coexisting intralobar and extralobar pulmonar y sequestrations. The anomaly causes a predisposition for pulmonary complications such as infection and hemoptysis. Extralobar sequestration is a rare congenital anomaly that consists of pulmonary tissue anatomically separate from normal lung and usually deriving its blood supply from systemic vessels. Abstract a 4yearold male presented with abdominal pain. There are two types of sequestrations, intralobar and extralobar.
Extralobar sequestration, elective resection, asymptomatic malformation. Journal of the society of laparoendoscopic surgeons, volume 16. Although there are numerous reports in the literature by surgeons who have encountered anomalous arteries arising from either. If so, share your ppt presentation slides online with. We report the management of a 34 year old male patient with a long. It is the commoner type of pulmonary sequestration four times commoner than extralobar sequestration, accounting for 75% of all sequestrations and is characterized by the sequestration surrounded by normal lung tissue without its own pleural covering. Extralobar sequestration is in conformity with a true accessory lung, with its own pleural envelope and accounts for 15%25% of all pulmonary sequestrations. Extralobar pulmonary sequestration is the less common type of pulmonary sequestration, accounting only for 1525%. Intradiaphragmatic extralobar pulmonary sequestration in adult. Extralobar pulmonary sequestration mimicking an adrenal. Torsion of pulmonary extralobar sequestration is extremely rare in childhood and adolescence, and as it presents with a variety of symptoms ranging from intermittent pain to fever from infarction, differential diagnosis is necessary. Extralobar diaphragmatic sequestration of the lung.
A computed tomography scan of the abdomen was negative, but a pleural effusion and mass was noted in the lower left thorax. In the same patient, extralobar pulmonary sequestration was detected and resected. Edward araujo junior,1,2 and sebastiao marques zanforlin filho1. Herein, we report a rare case of yearold girl who presented with abdominal pain and fever was diagnosed as infarction of torsed extralobar pulmonary. Two forms of pulmonary sequestration are described, intralobar and extralobar. Unilateral coexisting intralobar and extralobar pulmonary. Secuestro pulmonar extralobar asociado a malformacion. The finding of an accessory lung can alert the astute. Pulmonary sequestrations were divided into two types, intralobar sequestration 83. This sequestered tissue is therefore not connected to the normal bronchial airway architecture, and fails to function in, and contribute to, respiration of the organism.
Uniportal thoracoscopic lobectomy for intralobar pulmonary. Lectura sistematica by diego torres cardenas on prezi. Prenatal diagnosis of fetal intraabdominal extralobar pulmonary sequestration. Lobulillo pulmonar secundario by prezi user on prezi. It accounts for a small portion of pulmonary malformations 1,2. Read imaging of extralobar pulmonary sequestration in a patient with tetralogy of fallot with pulmonary atresia, ventricular septal defect and multiple aorto. Pulmonary sequestration is a congenital malformation representing an area of nonfunctional pulmonary tissue, not communicating with the bronchial tree and supplied by one or more systemic arteries.
Pdf treatment strategies for pulmonary sequestration in. Extralobar sequestration of pulmonary tissues is relatively rare and seldom produces symptoms. We report a unique extralobar pulmonary sequestration in the upper thoracic region with 3 aberrant vessels connecting to the right subclavian artery, right superior pulmonary vein, and right pulmonary artery in a 20yearold man. Els receives vascular supply mainly from the aorta thoracic or abdominal or from other arterial vessels splenic, subclavian, gastric, intercostal or. Endovascular treatment of pulmonary sequestration in. Pulmonary sequestrations may be defined as intralobular or extralobular, depending on their location. Read prenatal diagnosis of an extralobar pulmonary sequestration, archives of gynecology and obstetrics on deepdyve, the largest online rental service for scholarly research with thousands of academic publications available at your fingertips.